Table 2 Clinical data entries of the cohort
Parameter | Specific categories |
|---|---|
Identification Data | Patient code, Date of birth, Registered date |
Sex, Postal code, Height & Weight | |
Onset | Year of first symptom/first hospital visit/PAH diagnosis |
WHO functional class at diagnosis | Class I-IV |
Symptoms at diagnosis | Dyspnea/Chest pain/ |
Syncope/Edema/Palpitation/Weakness/Other(specify) | |
Signs at diagnosis | Cardiac murmur/Hepatomegaly/Elevated JVP/Pitting edema/Ascites |
Vital sign at diagnosis | Blood pressure-Heart rate-Respiratory rate-Body temperature |
PAH family history | Y/N, Specify |
Medical history | Connective tissue disease, Congenital heart disease |
PAH inducing drug history, HIV diagnosis/treatment history, Chronic hepatic disease | |
6MWT | Distance (meters), Blood pressure (before & after), |
Pulse rate, O2 Saturation | |
Blood Chemistry and Hemodynamics | NT-proBNP, troponin I, PT, Cr, |
Electrocardiogram | Normal, RVH, nonspecific |
Imaging studies | Chest radiography, Echocardiography, Computed chest tomography, Cardiac MRI |
Cardiopulmonary exercise test | pCO2, VE/VCO2, VO2/HR, peak VO2 |
RHC | Systolic, diastolic, mean pulmonary arterial pressure, pulmonary wedge pressure, right heart pressure, central vein, SvO2%, Pulmonary vascular resistance |